Table 1. Baseline Characteristics and the Yamaguchi Criteria.

From: Association between Relative Bradycardia and Adult-onset Still Disease

Overall (N = 8)
Baseline characteristics  
Age
Mean [Min, Q1, Median, Q3, Max] 59.9 [30.0, 43.0, 65.5, 71.0, 90.0]
Sex
Female 5 (62.5%)
Male 3 (37.5%)
Underlying disease
Cataract, Glaucoma 1 (12.5%)
Depression, Hypertension, Hyperlipidemia, Uterine cervix cancer 1 (12.5%)
Femoral neck fracture 1 (12.5%)
Knee prosthesis, DM, Hypertension 1 (12.5%)
Rheumatoid arthritis, Hyperlipidemia 1 (12.5%)
Sinusitis 1 (12.5%)
None 2 (25.0%)
Yamaguchi criteria
Major-1: Temperature >39℃ 1w
Yes 8 (100%)
No 0 (0%)
Major-2: Arthralgia or arthritis 2w
Yes 7 (87.5%)
No 1 (12.5%)
Major-3: Typical rash
Yes 4 (50.0%)
No 4 (50.0%)
Major-4: Leukocytosis >10000 with 80% polymorphonuclear cells
Yes 6 (75.0%)
No 2 (25.0%)
Minor-1: Sore throat
Yes 7 (87.5%)
No 1 (12.5%)
Minor-2: Lymphadenopathy or splenomegaly
Yes 1 (12.5%)
No 7 (87.5%)
Minor-3: Abnormal liver function test
Yes 8 (100%)
No 0 (0%)
Minor-4: Negative tests for ANA and RF
Yes 7 (87.5%)
No 1 (12.5%)
Table 2. Clinical Manifestation and Laboratory Data.

From: Association between Relative Bradycardia and Adult-onset Still Disease

Overall participants (N = 8)
Hospitalization
Number of days from onset to hospitalization
Mean [Min, Q1, Median, Q3, Max] 9.25 [2.0, 2.5, 11.5, 14.0, 15.0]
Number of days from onset to diagnosis
Mean [Min, Q1, Median, Q3, Max] 13.4 [3.0, 7.25, 15.0, 18.5, 21.0]
Vital sign and relative bradycardia
Body temperature on admission
Mean [Min, Q1, Median, Q3, Max] 38.3 [36.6, 37.8, 38.5, 39.2, 39.2]
Pulse rate on admission
Mean [Min, Q1, Median, Q3, Max] 93.1 [75.0, 84.5, 93.0, 104, 110]
Relative bradycardia on admission
Yes 5 (62.5%)
No 3 (37.5%)
Relative bradycardia after day 2 of hospitalization
Yes 8 (100%)
No 0 (0%)
Clinical manifestation and laboratory data
Spiking fever
Yes 8 (100%)
No 0 (0%)
Rigor
Yes 1 (12.5%)
No 7 (87.5%)
Headache
Yes 3 (37.5%)
No 5 (62.5%)
Ferritin (ng/mL)
Mean [Min, Q1, Median, Q3, Max] 16332 [552, 2355, 4682, 15881, 89430]
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